[Dislocation of the hip in a patient with von Recklinghausen disease].

نویسندگان

  • A Del Bosque-Herrero
  • L Ezquerra-Herrando
  • J Albareda-Albareda
چکیده

Neurofibromatosis type 1 (NF-1) is one of the most common autosomal dominant disorders affecting humans. Patients with NF-1 may present with characteristic orthopaedic manifestations such as scoliosis, congenital pseudoarthrosis and limb hyperttrophy. Dislocation of the hip associated with NF-1 is a rare occurrence. There is a relative paucity of reported cases of pathological hip dislocation in patients with NF-1, with 13 documented cases found in the published literature. Seven dislocations occurred following trivial trauma and 6 cases were deemed atraumatic. We report a case of hip dislocation in a 26 years old male with NF-1 and scoliosis, that was treated successfully by closed reduction and skin traction.

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عنوان ژورنال:
  • Revista espanola de cirugia ortopedica y traumatologia

دوره 58 4  شماره 

صفحات  -

تاریخ انتشار 2014